Hypertrophic cardiomyopathy is the single most common form of inherited heart disease. Left ventricular outflow tract obstruction (LVOTO) is a recognised feature of this condition which arises when blood leaving the outflow tract is impeded by systolic anterior motion of the mitral valve. In an important minority of patients, breathlessness, chest pain and syncope may result and persist despite the use of medications. In suitable candidates, surgery may relieve obstruction and its associated symptoms, and normalise life expectancy. Refinements in surgical techniques have marked improvements in the understanding of mechanisms underlying LVOTO. In this review, we hope to provide the reader with an understanding of how contemporary surgical practice has developed, which patients should be considered for surgery, and what results are anticipated. The role echocardiography plays in this area is highlighted throughout.
Neil Howell and William Bradlow
Lauren Turvey, Daniel X Augustine, Shaun Robinson, David Oxborough, Martin Stout, Nicola Smith, Allan Harkness, Lynne Williams, Richard P Steeds, and William Bradlow
Hypertrophic cardiomyopathy (HCM) is common, inherited and characterised by unexplained thickening of the myocardium. The British Society of Echocardiography (BSE) has recently published a minimum dataset for transthoracic echocardiography detailing the core views needed for a standard echocardiogram. For patients with confirmed or suspected HCM, additional views and measurements are necessary. This guideline, therefore, supplements the minimum dataset and describes a tailored, stepwise approach to the echocardiographic examination, and echocardiography’s position in the diagnostic pathway, before advising on the imaging of disease complications and invasive treatments.